A case of Prader-Willi Syndrome with Behavioural Disturbances: a successful multidisciplinary management approach

Md Rosli, Najwa Hanim and Md Tahir, Mohd Faiz (2020) A case of Prader-Willi Syndrome with Behavioural Disturbances: a successful multidisciplinary management approach. Jurnal of Clinical and Health Sciences, 5 (1). pp. 83-86. E-ISSN 0127-984X

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Abstract

Prader-Willi Syndrome (PWS) is a genetically determined neurodevelopmental disorder occurring in 1 in 15,000 births. PWS is a rare case in Malaysia and a successful approach to its management has not been well reported here. We present a case of a 13-year-old boy with Prader-Willi Syndrome with prominent behavioural disturbances characterised by temper tantrums, compulsive food intake, stubbornness, stealing and impulsivity further complicated by underlying morbid obesity, poorly controlled type 2 diabetes mellitus, hypertension, dyslipidaemia, obstructive sleep apnoea syndrome and intellectual disability. Multidisciplinary approach involving child and adolescent psychiatrist, occupational therapist, counsellor, family therapist, endocrinologist and dietician has shown to improve the patient’s weight, glucose and blood pressure control and most importantly the behavioural disturbances.

Item Type:	Article (Case Report)
Additional Information:	5698/81233
Uncontrolled Keywords:	Prader-Willi Syndrome, adolescent, temper tantrums, behaviour disturbances, intellectual disability
Subjects:	R Medicine > R Medicine (General)
Kulliyyahs/Centres/Divisions/Institutes (Can select more than one option. Press CONTROL button):	Kulliyyah of Medicine > Department of Psychiatry
Depositing User:	Dr Najwa Hanim Md Rosli
Date Deposited:	06 Jul 2020 16:22
Last Modified:	06 Jul 2020 16:22
URI:	http://irep.iium.edu.my/id/eprint/81233

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