A case of lymphangioleiomyomatosis with multiple angiomyolipomas in the kidneys: a case report

How, Soon Hin and Sa'at@Yusof, Azlin and Pang, Yong-Kek and Liam, Chong-Kin (2006) A case of lymphangioleiomyomatosis with multiple angiomyolipomas in the kidneys: a case report. Journal of Health and Translational Medicine, 6 (2). pp. 35-38. ISSN 2289-392X (O), 1823-7339 (P)

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Abstract

Lymphangioleiomyomatosis (LAM) is a rare disease. The reported prevalence is around one per million in the West but the exact prevalence in Asia is unknown. It affects primarily young women of reproductive age, with a mean age of onset at 34 years. The disease is characterised by an abnormal proliferation of smooth muscle-like cells that grow over a course of time to obstruct airways, lymphatic and blood vessels. We report a case of LAM in a young woman who presented with a spontaneous pneumothorax. Computed tomography scan of the thorax and abdomen showed homogenous thin-walled cystic lesions with normal intervening lung parenchyma and multiple lesions in her kidneys with Hounsfield units similar to that of fat.

Item Type:	Article (Journal)
Additional Information:	2987/44330
Uncontrolled Keywords:	Lymphangioleiomyomatosis, renal angiomyolipoma, spontaneous pneumothorax, cystic lesions of lungs
Subjects:	R Medicine > R Medicine (General)
Kulliyyahs/Centres/Divisions/Institutes (Can select more than one option. Press CONTROL button):	Kulliyyah of Medicine > Department of Internal Medicine
Depositing User:	Miss Noor Shafiruz Ahmad
Date Deposited:	21 Aug 2015 09:40
Last Modified:	21 Aug 2015 09:40
URI:	http://irep.iium.edu.my/id/eprint/44330

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