Renal cell carcinoma in a von Hippel-Lindau syndrome; when should pheochromocytoma be anticipated?

Mohd Shah, Azarisman Shah and K, Nor Azmi (2007) Renal cell carcinoma in a von Hippel-Lindau syndrome; when should pheochromocytoma be anticipated? Singapore Medical Journal, 48(8) (779). ISSN 0037-5675

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Abstract

A 39-year-old man was diagnosed with von Hippel-Lindau syndrome, which was associated with retinal haemangioblastoma, cervical cord haemangioblastoma and bilateral renal cell carcinoma. He subsequently underwent an arterial embolisation and cervical laminectomy, following a spinal angiogram of the cervical lesion. He also had a right radical nephrectomy, with no perioperative complications. However, on admission for the left radical nephrectomy, he was noted to have preoperative hypertension. Further investigation revealed an enlarged left adrenal gland on abdominal computed tomography scan and raised urinary catecholamines. We discuss the risk of renal cell carcinoma a nd ph a e oc h romoc y toma a r i s ing concomitantly in von Hippel-Lindau syndrome, and how best to investigate and manage them.

Item Type:	Article (Journal)
Additional Information:	3808/17108
Uncontrolled Keywords:	phaeochromocytoma, renal cell carcinoma, von Hippel-Lindau Syndrome
Subjects:	R Medicine > RC Internal medicine > RC254 Neoplasms. Tumors. Oncology (including Cancer)
Kulliyyahs/Centres/Divisions/Institutes (Can select more than one option. Press CONTROL button):	Kulliyyah of Medicine > Department of Internal Medicine
Depositing User:	Mr iskhandar adnan
Date Deposited:	26 Jan 2012 14:54
Last Modified:	26 Jan 2012 17:31
URI:	http://irep.iium.edu.my/id/eprint/17108

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