Renal artery fibromuscular dysplasia: diagnostic challenges in a child presenting with hyponatremic hypertensive syndrome (HHS)

Abu Bakar, Asrar and Syed Ahmad Shihabuddin Abdurrahman Alsagoff, Sharifah Aishah and Anuar, Muhamad Azamin and Durai Raja Lingam, Ganeshwara (2024) Renal artery fibromuscular dysplasia: diagnostic challenges in a child presenting with hyponatremic hypertensive syndrome (HHS). Journal of Pediatric and Neonatal Individualized Medicine (JPNIM), 13 (1). pp. 1-7. ISSN 2281-0692

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Abstract

A 2-year-9-month-old boy presented with renovascular hypertension caused by middle-segment stenosis of the right renal artery, and a severe hypertensive crisis, accompanied by hyponatremia, hypokalemia, and transient proteinuria. Fibromuscular dysplasia (FMD) is the most common cause of renovascular disease in children. However, the diagnosis of FMD is often delayed because findings on renal sonograms with Doppler are frequently missed. A high index of suspicion is required to further investigate a renovascular cause when persistent hypertension in a child cannot be otherwise explained. We present the challenges of reaching a diagnosis in a resource-limited setting and discuss how a multidisciplinary approach was key to successfully manage a young child with renovascular disease.

Item Type:	Article (Case Report)
Uncontrolled Keywords:	Fibromuscular dysplasia, renovascular disease, hyponatremic hypertensive syndrome, renal artery stenosis, childhood hypertension.
Subjects:	R Medicine > RJ Pediatrics R Medicine > RJ Pediatrics > RJ370 Disease of children R Medicine > RJ Pediatrics > RJ50 Examination. Diagnosis R Medicine > RJ Pediatrics > RJ58 Clinical cases
Kulliyyahs/Centres/Divisions/Institutes (Can select more than one option. Press CONTROL button):	Kulliyyah of Medicine > Department of Paediatrics Kulliyyah of Medicine
Depositing User:	Dr Muhamad Azamin Anuar
Date Deposited:	13 Mar 2024 11:03
Last Modified:	13 Mar 2024 11:03
URI:	http://irep.iium.edu.my/id/eprint/110550

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